Maple syrup urine disease (MSUD) || Metabolism of Valine, Leucine, Isoleucine ||NEET PG Biochemistry

This is the video on metabolism of branched chain amino acids with NEET PG and AIIMS MCQs. Valine, Isoleucine and leucine are branched essential amino acids 1. Valine: Glucogenic 2. Isoleucine : Both glucogenic and ketogenic 3. Leucine: Ketogenic Metabolic Disorder of Branched Chain Amino Acids are Maple syrup urine disease (MSUD) or branched chain keto aciduria and Isovaleric Aciduria